Inforzato HCB*, Raizer C and Storion MA
Department of Plastic Surgery, University Federal of São Paulo, BrazilFulltext PDF
The Aplasia Cutis Congenita (ACC) is a rare malformation, and it does characterize by the absence of skin layers and subcutaneous cellular tissue. It occurs most frequently in the scalp region, but can affect any anatomical region; the incidence is in between 0.5 to 1 of 10,000 live births being more common in female gender. The etiology may be associated with Epidermolysis Bullosa (EB), intrauterine infections, ectodermal dysplasia; it may be associated with chromosomal anomalies such as trisomy 13, and also with the autosomal recessive and dominant inheritance in 35% to 50% of cases. To report the case of a patient with ACC in the lower limbs treated exclusively with biological dressing.
Aplasia; Cutis anomaly; Epidermolysis bullosa
Inforzato HCB, Raizer C, Storion MA. Conservative Treatment for Single Wound due to Aplasia Cutis Congenita Type IV ( Bart’s Syndrome) in the Lower Limb: Case Report. Clin Case Rep Int. 2021; 5: 1249.