Recurrent Orbital Myxofibrosarcoma: Case Report and Review of Literature

Camila Sanhueza, María Josefina Fry, and Eugenia Abusleme

Department of Ophthalmology, Pontifical Catholic University of Chile, Chile

^*Correspondance to: Camila Sanhueza 

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Abstract:

Myxofibrosarcoma in orbital location is extremely rare. There are less than 10 reported cases of orbital myxofibrosarcoma. The authors report a case of a patient with a previous resected low-grade myxofibrosarcoma in the right orbit, who 16-years later presented with the same tumor. This first recurrence was resected, leaving a residual mass. Two years later, the patient presented with an extensive mass in the right orbit, sinuses, and nasal cavities. The histopathological examination showed high-grade myxofibrosarcoma. The patient underwent palliative radiotherapy and palliative care. The risk of metastasis of this type of tumor depends on the degree of histological differentiation. But local recurrence rate is similar for all with an increase of metastasis risk with every recurrence. Due to the few cases reported there are no standardized management guidelines. However, it is recommended wide surgical margins be associated with postoperative radiotherapy in the presence of residual lesions or high-grade tumors.

Keywords:

Myxofibrosarcoma; Orbital; Proptosis

Cite the Article:

Sanhueza C, Fry MJ, Abusleme E. Recurrent Orbital Myxofibrosarcoma: Case Report and Review of Literature. Clin Case Rep Int. 2022; 6: 1326.