Cystic Fibrosis with Pancreatic Insufficiency: A Case Report

Luthfun Nahar, Bazlul Karim, Afsana Yasmin, Subarna Rani Das, Kamrun Nahar and Parisa Marjan

Department of Pediatric Gastroenterology and Nutrition, Bangabandhu Sheikh Mujib Medical University, Bangladesh

^*Correspondance to: Luthfun Nahar 

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Abstract:

Cystic fibrosis is an autosomal recessive disorder; the main responsible gene is Cystic Fibrosis Transmembrane conductance Regulator (CFTR) which is located on long arm of chromosome. Mutation of this gene encoding CFTR protein results cystic fibrosis. This disease involves multiple systems of body as respiratory, gastrointestinal, hepatobiliary, pancreatic, genitourinary and sweat duct. Pancreatic insufficiency presents with symptoms when >95% exocrine function is lost. It is associated about 85% in patient of cystic fibrosis which indicate poor prognosis. This paper presents a case of cystic fibrosis with pancreatic insufficiency and chronic pancreatitis with osteoporosis.

Keywords:

Cystic fibrosis; Pancreatitis; Pancreatic insufficiency; Growth failure

Cite the Article:

Nahar L, Karim B, Yasmin A, Rani Das S, Nahar K, Marjan P. Cystic Fibrosis with Pancreatic Insufficiency: A Case Report. Clin Case Rep Int. 2020; 4: 1139.