Fibrosarcomatous Transformation of Dermatofibrosarcoma Protuberans (DFSP) - An Aggressive Variant Presenting as Abdominal Mass

Jameel JKA, Sunil N, Loganathan G and Reddy PK

Department of Surgical Gastroenterology and Minimal Access Surgery, Apollo Hospitals, India

^*Correspondance to: Jainudeen KA Jameel 

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Abstract:

Dermatofibrosarcoma Protuberans (DFSP) is a slow growing mesenchymal tumour arising from dermal fibroblasts. It usually occurs in middle-aged population and starts as a firm plaque-like lesion and is most commonly seen in the trunk. When there is a fibromatous transformation within the DFSP, the lesion can rapidly increase in size and develop an increased metastatic potential. Treatment of choice for DFSP is surgical excision with negative margins. Adjuvant therapy is indicated based on the margin status and aggressiveness of the tumor. Here we present a patient with a large DFSP with fibromatous transformation which presented as a large abdominal wall mass with gross extension into the peritoneal cavity, which was successfully excised.

Keywords:

Dermatofibrosarcoma protuberans; Abdominal mass; Fibromatous transformation; Excision

Cite the Article:

Jameel JKA, Sunil N, Loganathan G, Reddy PK. Fibrosarcomatous Transformation of Dermatofibrosarcoma Protuberans (DFSP) - An Aggressive Variant Presenting as Abdominal Mass. Clin Case Rep Int. 2022; 6: 1291.