IgG4-Related Disease with Pancreas and Skin Involvement: Case Report and Review of Literature

Xiao C, Lu T and Huang X

Department of Rheumatology, Tongji University School of Medicine and Shanghai East Hospital, China

^*Correspondance to: Xinfang Huang 

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Abstract:

Immunoglobulin G4-Related Disease (IgG4-RD) is an autoimmune inflammatory disease characterized by infiltration of IgG4+ plasma cells, which can affect multiple organs such as pancreas, biliary tract, kidneys, salivary glands, lymph nodes, aorta, and retroperitoneum, et al. Cutaneous lesion involvement is a rare clinical manifestation of IgG4-RD. We report a case of IgG4-RD presenting with cutaneous lesions in combination with autoimmune pancreatitis and subacute thyroiditis. A skin biopsy pathology confirmed the diagnosis of IgG4-RD. Here we present an uncommon case of IgG4-RD with subacute thyroiditis with pancreatic and skin involvement and provide a brief literature review of skin manifestations and treatment.

Keywords:

Autoimmune pancreatitis; IgG4-related disease; Rash Skin pathology

Cite the Article:

Xiao C, Lu T, Huang X. IgG4-Related Disease with Pancreas and Skin Involvement: Case Report and Review of Literature. Clin Case Rep Int. 2023; 7: 1607.